Publications
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“Axonal Transport Defect in Gigaxonin Deficiency Rescued by Tubastatin A.”, Neurotherapeutics, vol. 20, no. 4, pp. 1215-1228, 2023.
“Distinct Plasma Immune Profile in ALS Implicates sTNFR-II in pAMPK/Leptin Homeostasis.”, Int J Mol Sci, vol. 24, no. 6, 2023.
“Emerging Trends in the Field of Inflammation and Proteinopathy in ALS/FTD Spectrum Disorder.”, Biomedicines, vol. 11, no. 6, 2023.
“The Mobility of Neurofilaments in Mature Myelinated Axons of Adult Mice.”, eNeuro, vol. 10, no. 3, 2023.
“A New Mouse Model of Giant Axonal Neuropathy with Overt Phenotypes and Neurodegeneration Driven by Neurofilament Disorganization.”, J Neurosci, vol. 43, no. 22, pp. 4174-4189, 2023.
“Transactive response DNA-binding protein 43 is enriched at the centrosome in human cells.”, Brain, vol. 146, no. 9, pp. 3624-3633, 2023.
“Ultrasensitive digital immunoassays for SOD1 conformation in amyotrophic lateral sclerosis.”, Bioanalysis, vol. 15, no. 15, pp. 927-936, 2023.
“Neurofilament Transport Is Bidirectional .”, eNeuro, vol. 9, no. 4, 2022.
“Noise-induced hearing loss vulnerability in type III intermediate filament peripherin gene knockout mice.”, Front Neurol, vol. 13, p. 962227, 2022.
, “Induction of autophagy mitigates TDP-43 pathology and translational repression of neurofilament mRNAs in mouse models of ALS/FTD.”, Mol Neurodegener, vol. 16, no. 1, p. 1, 2021.
, “Targeting TDP-43 Pathology Alleviates Cognitive and Motor Deficits Caused by Chronic Cerebral Hypoperfusion.”, Neurotherapeutics, vol. 18, no. 2, pp. 1095-1112, 2021.
, “TDP-43 triggers immune response via mitochondrial DNA release.”, Cell Res, vol. 31, no. 4, pp. 379-380, 2021.
, “Withaferin-A Treatment Alleviates TAR DNA-Binding Protein-43 Pathology and Improves Cognitive Function in a Mouse Model of FTLD.”, Neurotherapeutics, vol. 18, no. 1, pp. 286-296, 2021.
, “Mitigation of ALS Pathology by Neuron-Specific Inhibition of Nuclear Factor Kappa B Signaling.”, J Neurosci, vol. 40, no. 26, pp. 5137-5154, 2020.
, “Monoclonal full-length antibody against TAR DNA-binding protein 43 reduces related proteinopathy in neurons.”, JCI Insight, 2020.
, “Neurofilaments: neurobiological foundations for biomarker applications.”, Brain, vol. 143, no. 7, pp. 1975-1998, 2020.
, “Transmission of ALS pathogenesis by the cerebrospinal fluid”, Acta neuropathologica communications, vol. 8, no. 1, pp. 65 - 65, 2020.
, “Transmission of ALS pathogenesis by the cerebrospinal fluid.”, Acta Neuropathol Commun, vol. 8, no. 1, p. 65, 2020.
, “Key role of UBQLN2 in pathogenesis of amyotrophic lateral sclerosis and frontotemporal dementia.”, Acta Neuropathol Commun, vol. 7, no. 1, p. 103, 2019.
, “Local Acceleration of Neurofilament Transport at Nodes of Ranvier.”, J Neurosci, vol. 39, no. 4, pp. 663-677, 2019.
, “Virus-mediated delivery of antibody targeting TAR DNA-binding protein-43 mitigates associated neuropathology.”, J Clin Invest, vol. 129, no. 4, pp. 1581-1595, 2019.
, “Chronic Administration of Pimozide Fails to Attenuate Motor and Pathological Deficits in Two Mouse Models of Amyotrophic Lateral Sclerosis.”, Neurotherapeutics, vol. 15, no. 3, pp. 715-727, 2018.
, “Misfolded SOD1 pathology in sporadic Amyotrophic Lateral Sclerosis.”, Sci Rep, vol. 8, no. 1, p. 14223, 2018.
, “Neurofilament light interaction with GluN1 modulates neurotransmission and schizophrenia-associated behaviors.”, Transl Psychiatry, vol. 8, no. 1, p. 167, 2018.
