Publications
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, “Overexpressed wild-type superoxide dismutase 1 exhibits amyotrophic lateral sclerosis-related misfolded conformation in induced pluripotent stem cell-derived spinal motor neurons.”, Neuroreport, vol. 29, no. 1, pp. 25-29, 2018.
, “Protective effects of Withania somnifera extract in SOD1 mouse model of amyotrophic lateral sclerosis.”, Exp Neurol, vol. 309, pp. 193-204, 2018.
, “Neuroleptics as therapeutic compounds stabilizing neuromuscular transmission in amyotrophic lateral sclerosis.”, JCI Insight, vol. 2, no. 22, 2017.
, “The Src/c-Abl pathway is a potential therapeutic target in amyotrophic lateral sclerosis.”, Sci Transl Med, vol. 9, no. 391, 2017.
, “Withania somnifera Reverses Transactive Response DNA Binding Protein 43 Proteinopathy in a Mouse Model of Amyotrophic Lateral Sclerosis/Frontotemporal Lobar Degeneration.”, Neurotherapeutics, vol. 14, no. 2, pp. 447-462, 2017.
, “Exosome secretion is a key pathway for clearance of pathological TDP-43.”, Brain, vol. 139, no. Pt 12, pp. 3187-3201, 2016.
, “From animal models to human disease: a genetic approach for personalized medicine in ALS.”, Acta Neuropathol Commun, vol. 4, no. 1, p. 70, 2016.
, “Intermediate filament aggregates cause mitochondrial dysmotility and increase energy demands in giant axonal neuropathy.”, Hum Mol Genet, 2016.
, “MTHFSD and DDX58 are novel RNA-binding proteins abnormally regulated in amyotrophic lateral sclerosis.”, Brain, vol. 139, no. Pt 1, pp. 86-100, 2016.
, “Neurofilament depletion improves microtubule dynamics via modulation of Stat3/stathmin signaling.”, Acta Neuropathol, vol. 132, no. 1, pp. 93-110, 2016.
, “Sex-dependent effects of chromogranin B P413L allelic variant as disease modifier in amyotrophic lateral sclerosis.”, Hum Mol Genet, 2016.
, “Sex-dependent effects of chromogranin B P413L allelic variant as disease modifier in amyotrophic lateral sclerosis.”, Hum Mol Genet, vol. 25, no. 21, pp. 4771-4786, 2016.
, “CD11b+Ly6G- myeloid cells mediate mechanical inflammatory pain hypersensitivity.”, Proc Natl Acad Sci U S A, vol. 112, no. 49, pp. E6808-17, 2015.
, “Dissociation of Axonal Neurofilament Content from Its Transport Rate.”, PLoS One, vol. 10, no. 7, p. e0133848, 2015.
, “Early and persistent abnormal decoding by glial cells at the neuromuscular junction in an ALS model.”, J Neurosci, vol. 35, no. 2, pp. 688-706, 2015.
, “Early-stage treatment with Withaferin A reduces levels of misfolded superoxide dismutase 1 and extends lifespan in a mouse model of amyotrophic lateral sclerosis.”, Neurotherapeutics, vol. 12, no. 1, pp. 217-33, 2015.
, “Functions of neurofilaments in synapses.”, Mol Psychiatry, vol. 20, no. 8, p. 915, 2015.
, “Inflammation Induces TDP-43 Mislocalization and Aggregation.”, PLoS One, vol. 10, no. 10, p. e0140248, 2015.
, “Neurofilament subunits are integral components of synapses and modulate neurotransmission and behavior in vivo.”, Mol Psychiatry, vol. 20, no. 8, pp. 986-94, 2015.
, “Type II spiral ganglion afferent neurons drive medial olivocochlear reflex suppression of the cochlear amplifier.”, Nat Commun, vol. 6, p. 7115, 2015.
, “Ubiquilin-2 drives NF-κB activity and cytosolic TDP-43 aggregation in neuronal cells.”, Mol Brain, vol. 8, no. 1, p. 71, 2015.
, “Adeno-associated virus-mediated delivery of a recombinant single-chain antibody against misfolded superoxide dismutase for treatment of amyotrophic lateral sclerosis.”, Mol Ther, vol. 22, no. 3, pp. 498-510, 2014.
, “Interaction of transactive response DNA binding protein 43 with nuclear factor κB in mild cognitive impairment with episodic memory deficits.”, Acta Neuropathol Commun, vol. 2, p. 37, 2014.
, “Loss of glial neurofascin155 delays developmental synapse elimination at the neuromuscular junction.”, J Neurosci, vol. 34, no. 38, pp. 12904-18, 2014.
, “Axonal transport deficits and neurodegenerative diseases.”, Nat Rev Neurosci, vol. 14, no. 3, pp. 161-76, 2013.
