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Publications

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Filters: Author is J-P Julien  [Clear All Filters]
2012
Audet J-, Gowing G, Paradis R, Soucy G, J-P Julien. Ablation of proliferating cells in the CNS exacerbates motor neuron disease caused by mutant superoxide dismutase. PLoS ONE. 2012;7(4):e34932.
Swarup V, Audet J-, Phaneuf D, Kriz J, J-P Julien. Abnormal regenerative responses and impaired axonal outgrowth after nerve crush in TDP-43 transgenic mouse models of amyotrophic lateral sclerosis. J Neurosci. 2012;32(50):18186-95.
Zhu J-, J-P Julien, Dubi Y, Balatsky AV. Local electronic structure and Fano interference in tunneling into a Kondo hole system. Phys Rev Lett. 2012;108(18):186401.
Brotherton TE, Li Y, Cooper D, Gearing M, J-P Julien, Rothstein JD, et al. Localization of a toxic form of superoxide dismutase 1 protein to pathologically affected tissues in familial ALS. Proc Natl Acad Sci USA. 2012;109(14):5505-10.
Audet J-, Soucy G, J-P Julien. Methylene blue administration fails to confer neuroprotection in two amyotrophic lateral sclerosis mouse models. Neuroscience. 2012;209:136-43.
Gentil BJ, Minotti S, Beange M, Baloh RH, J-P Julien, Durham HD. Normal role of the low-molecular-weight neurofilament protein in mitochondrial dynamics and disruption in Charcot-Marie-Tooth disease. FASEB J. 2012;26(3):1194-203.
Yuan A, Sasaki T, Kumar A, Peterhoff CM, Rao MV, Liem RK, et al. Peripherin is a subunit of peripheral nerve neurofilaments: implications for differential vulnerability of CNS and peripheral nervous system axons. J Neurosci. 2012;32(25):8501-8.
2011
Swarup V, J-P Julien. ALS pathogenesis: recent insights from genetics and mouse models. Prog Neuropsychopharmacol Biol Psychiatry. 2011;35(2):363-9.
Swarup V, Phaneuf D, Dupré N, Petri S, Strong M, Kriz J, et al. Deregulation of TDP-43 in amyotrophic lateral sclerosis triggers nuclear factor κB-mediated pathogenic pathways. J Exp Med. 2011;208(12):2429-47.
Dequen F, Cairns NJ, Bigio EH, J-P Julien. Gigaxonin mutation analysis in patients with NIFID. Neurobiol Aging. 2011;32(8):1528-9.
Velde CV, McDonald KK, Boukhedimi Y, McAlonis-Downes M, Lobsiger CS, Hadj SB, et al. Misfolded SOD1 associated with motor neuron mitochondria alters mitochondrial shape and distribution prior to clinical onset. PLoS ONE. 2011;6(7):e22031.
Rao MV, Mohan PS, Kumar A, Yuan A, Montagna L, Campbell J, et al. The myosin Va head domain binds to the neurofilament-L rod and modulates endoplasmic reticulum (ER) content and distribution within axons. PLoS ONE. 2011;6(2):e17087.
Swarup V, Phaneuf D, Bareil C, Robertson J, Rouleau GA, Kriz J, et al. Pathological hallmarks of amyotrophic lateral sclerosis/frontotemporal lobar degeneration in transgenic mice produced with TDP-43 genomic fragments. Brain. 2011;134(Pt 9):2610-26.
Filali M, Dequen F, Lalonde R, J-P Julien. Sensorimotor and cognitive function of a NEFL(P22S) mutant model of Charcot-Marie-Tooth disease type 2E. Behav Brain Res. 2011;219(2):175-80.

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