Publications
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Filtres: Author is J-P Julien [Enlever les filtres]
, « Induction of autophagy mitigates TDP-43 pathology and translational repression of neurofilament mRNAs in mouse models of ALS/FTD. », Mol Neurodegener, vol. 16, nᵒ 1, p. 1, 2021.
, « Targeting TDP-43 Pathology Alleviates Cognitive and Motor Deficits Caused by Chronic Cerebral Hypoperfusion. », Neurotherapeutics, vol. 18, nᵒ 2, p. 1095-1112, 2021.
, « TDP-43 triggers immune response via mitochondrial DNA release. », Cell Res, vol. 31, nᵒ 4, p. 379-380, 2021.
, « Withaferin-A Treatment Alleviates TAR DNA-Binding Protein-43 Pathology and Improves Cognitive Function in a Mouse Model of FTLD. », Neurotherapeutics, vol. 18, nᵒ 1, p. 286-296, 2021.
, « Mitigation of ALS Pathology by Neuron-Specific Inhibition of Nuclear Factor Kappa B Signaling. », J Neurosci, vol. 40, nᵒ 26, p. 5137-5154, 2020.
, « Monoclonal full-length antibody against TAR DNA-binding protein 43 reduces related proteinopathy in neurons. », JCI Insight, 2020.
, « Neurofilaments: neurobiological foundations for biomarker applications. », Brain, vol. 143, nᵒ 7, p. 1975-1998, 2020.
, « Transmission of ALS pathogenesis by the cerebrospinal fluid », Acta neuropathologica communications, vol. 8, nᵒ 1, p. 65 - 65, 2020.
, « Transmission of ALS pathogenesis by the cerebrospinal fluid. », Acta Neuropathol Commun, vol. 8, nᵒ 1, p. 65, 2020.
, « Key role of UBQLN2 in pathogenesis of amyotrophic lateral sclerosis and frontotemporal dementia. », Acta Neuropathol Commun, vol. 7, nᵒ 1, p. 103, 2019.
, « Local Acceleration of Neurofilament Transport at Nodes of Ranvier. », J Neurosci, vol. 39, nᵒ 4, p. 663-677, 2019.
, « Virus-mediated delivery of antibody targeting TAR DNA-binding protein-43 mitigates associated neuropathology. », J Clin Invest, vol. 129, nᵒ 4, p. 1581-1595, 2019.
, « Chronic Administration of Pimozide Fails to Attenuate Motor and Pathological Deficits in Two Mouse Models of Amyotrophic Lateral Sclerosis. », Neurotherapeutics, vol. 15, nᵒ 3, p. 715-727, 2018.
, « Misfolded SOD1 pathology in sporadic Amyotrophic Lateral Sclerosis. », Sci Rep, vol. 8, nᵒ 1, p. 14223, 2018.
, « Neurofilament light interaction with GluN1 modulates neurotransmission and schizophrenia-associated behaviors. », Transl Psychiatry, vol. 8, nᵒ 1, p. 167, 2018.
, « Neuronal Expression of UBQLN2 Exacerbates TDP-43 Pathology in TDP-43 Mice through Interaction with Ubiquitin. », Mol Neurobiol, 2018.
, « Overexpressed wild-type superoxide dismutase 1 exhibits amyotrophic lateral sclerosis-related misfolded conformation in induced pluripotent stem cell-derived spinal motor neurons. », Neuroreport, vol. 29, nᵒ 1, p. 25-29, 2018.
, « Protective effects of Withania somnifera extract in SOD1 mouse model of amyotrophic lateral sclerosis. », Exp Neurol, vol. 309, p. 193-204, 2018.
, « Neuroleptics as therapeutic compounds stabilizing neuromuscular transmission in amyotrophic lateral sclerosis. », JCI Insight, vol. 2, nᵒ 22, 2017.
, « The Src/c-Abl pathway is a potential therapeutic target in amyotrophic lateral sclerosis. », Sci Transl Med, vol. 9, nᵒ 391, 2017.
, « Withania somnifera Reverses Transactive Response DNA Binding Protein 43 Proteinopathy in a Mouse Model of Amyotrophic Lateral Sclerosis/Frontotemporal Lobar Degeneration. », Neurotherapeutics, vol. 14, nᵒ 2, p. 447-462, 2017.
, « Exosome secretion is a key pathway for clearance of pathological TDP-43. », Brain, vol. 139, nᵒ Pt 12, p. 3187-3201, 2016.
, « From animal models to human disease: a genetic approach for personalized medicine in ALS. », Acta Neuropathol Commun, vol. 4, nᵒ 1, p. 70, 2016.
, « Intermediate filament aggregates cause mitochondrial dysmotility and increase energy demands in giant axonal neuropathy. », Hum Mol Genet, 2016.
, « MTHFSD and DDX58 are novel RNA-binding proteins abnormally regulated in amyotrophic lateral sclerosis. », Brain, vol. 139, nᵒ Pt 1, p. 86-100, 2016.
