Publications
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Filtres: Keyword is Motor Neurons [Enlever les filtres]
, « Normal Molecular Specification and Neurodegenerative Disease-Like Death of Spinal Neurons Lacking the SNARE-Associated Synaptic Protein Munc18-1. », J Neurosci, vol. 36, nᵒ 2, p. 561-76, 2016.
, « Neuroprotection through excitability and mTOR required in ALS motoneurons to delay disease and extend survival. », Neuron, vol. 80, nᵒ 1, p. 80-96, 2013.
, « Normal role of the low-molecular-weight neurofilament protein in mitochondrial dynamics and disruption in Charcot-Marie-Tooth disease. », FASEB J, vol. 26, nᵒ 3, p. 1194-203, 2012.
, « Misfolded SOD1 associated with motor neuron mitochondria alters mitochondrial shape and distribution prior to clinical onset. », PLoS One, vol. 6, nᵒ 7, p. e22031, 2011.
, « Extracellular mutant SOD1 induces microglial-mediated motoneuron injury. », Glia, vol. 58, nᵒ 2, p. 231-43, 2010.
, « Induction of protective immunity by vaccination with wild-type apo superoxide dismutase 1 in mutant SOD1 transgenic mice. », J Neuropathol Exp Neurol, vol. 69, nᵒ 10, p. 1044-56, 2010.
, « Neuronal over-expression of chromogranin A accelerates disease onset in a mouse model of ALS. », J Neurochem, vol. 115, nᵒ 5, p. 1102-11, 2010.
, « Ablation of proliferating microglia does not affect motor neuron degeneration in amyotrophic lateral sclerosis caused by mutant superoxide dismutase. », J Neurosci, vol. 28, nᵒ 41, p. 10234-44, 2008.
, « Als2 mRNA splicing variants detected in KO mice rescue severe motor dysfunction phenotype in Als2 knock-down zebrafish. », Hum Mol Genet, vol. 17, nᵒ 17, p. 2691-702, 2008.
, « Modest loss of peripheral axons, muscle atrophy and formation of brain inclusions in mice with targeted deletion of gigaxonin exon 1. », J Neurochem, vol. 107, nᵒ 1, p. 253-64, 2008.
, « Psychopathy and the mirror neuron system: preliminary findings from a non-psychiatric sample. », Psychiatry Res, vol. 160, nᵒ 2, p. 137-44, 2008.
, « Disruption of neurofilament network with aggregation of light neurofilament protein: a common pathway leading to motor neuron degeneration due to Charcot-Marie-Tooth disease-linked mutations in NFL and HSPB1. », Hum Mol Genet, vol. 16, nᵒ 24, p. 3103-16, 2007.
, « Manipulation of protein kinases reveals different mechanisms for upregulation of heat shock proteins in motor neurons and non-neuronal cells. », Mol Cell Neurosci, vol. 34, nᵒ 1, p. 20-33, 2007.
, « Wild-type superoxide dismutase acquires binding and toxic properties of ALS-linked mutant forms through oxidation. », J Neurochem, vol. 102, nᵒ 1, p. 170-8, 2007.
, « Chromogranin-mediated secretion of mutant superoxide dismutase proteins linked to amyotrophic lateral sclerosis. », Nat Neurosci, vol. 9, nᵒ 1, p. 108-18, 2006.
, « Clinical implications of cross-system interactions. », Semin Speech Lang, vol. 27, nᵒ 4, p. 300-9, 2006.
, « Linear summation of cat motor cortex outputs. », J Neurosci, vol. 26, nᵒ 20, p. 5574-81, 2006.
, « Transgenic mouse models of amyotrophic lateral sclerosis. », Biochim Biophys Acta, vol. 1762, nᵒ 11-12, p. 1013-24, 2006.
, « Cytoskeletal defects in amyotrophic lateral sclerosis (motor neuron disease). », Novartis Found Symp, vol. 264, p. 183-92; discussion 192-6, 227-30, 2005.
, « On the potential role of the corticospinal tract in the control and progressive adaptation of the soleus h-reflex during backward walking. », J Neurophysiol, vol. 94, nᵒ 2, p. 1133-42, 2005.
, « Exacerbation of motor neuron disease by chronic stimulation of innate immunity in a mouse model of amyotrophic lateral sclerosis. », J Neurosci, vol. 24, nᵒ 6, p. 1340-9, 2004.
, « Cell cycle regulators in the neuronal death pathway of amyotrophic lateral sclerosis caused by mutant superoxide dismutase 1. », J Neurosci, vol. 23, nᵒ 6, p. 2131-40, 2003.
, « Efficient three-drug cocktail for disease induced by mutant superoxide dismutase. », Ann Neurol, vol. 53, nᵒ 4, p. 429-36, 2003.
, « Peripherin is not a contributing factor to motor neuron disease in a mouse model of amyotrophic lateral sclerosis caused by mutant superoxide dismutase. », Neurobiol Dis, vol. 13, nᵒ 2, p. 158-66, 2003.
, « Peripherin-mediated death of motor neurons rescued by overexpression of neurofilament NF-H proteins. », J Neurochem, vol. 85, nᵒ 1, p. 248-56, 2003.
