Publications
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Filtres: Author is J-P Julien [Enlever les filtres]
, « Overexpressed wild-type superoxide dismutase 1 exhibits amyotrophic lateral sclerosis-related misfolded conformation in induced pluripotent stem cell-derived spinal motor neurons. », Neuroreport, vol. 29, nᵒ 1, p. 25-29, 2018.
, « Protective effects of Withania somnifera extract in SOD1 mouse model of amyotrophic lateral sclerosis. », Exp Neurol, vol. 309, p. 193-204, 2018.
, « Neuroleptics as therapeutic compounds stabilizing neuromuscular transmission in amyotrophic lateral sclerosis. », JCI Insight, vol. 2, nᵒ 22, 2017.
, « The Src/c-Abl pathway is a potential therapeutic target in amyotrophic lateral sclerosis. », Sci Transl Med, vol. 9, nᵒ 391, 2017.
, « Withania somnifera Reverses Transactive Response DNA Binding Protein 43 Proteinopathy in a Mouse Model of Amyotrophic Lateral Sclerosis/Frontotemporal Lobar Degeneration. », Neurotherapeutics, vol. 14, nᵒ 2, p. 447-462, 2017.
, « Exosome secretion is a key pathway for clearance of pathological TDP-43. », Brain, vol. 139, nᵒ Pt 12, p. 3187-3201, 2016.
, « From animal models to human disease: a genetic approach for personalized medicine in ALS. », Acta Neuropathol Commun, vol. 4, nᵒ 1, p. 70, 2016.
, « Intermediate filament aggregates cause mitochondrial dysmotility and increase energy demands in giant axonal neuropathy. », Hum Mol Genet, 2016.
, « MTHFSD and DDX58 are novel RNA-binding proteins abnormally regulated in amyotrophic lateral sclerosis. », Brain, vol. 139, nᵒ Pt 1, p. 86-100, 2016.
, « Neurofilament depletion improves microtubule dynamics via modulation of Stat3/stathmin signaling. », Acta Neuropathol, vol. 132, nᵒ 1, p. 93-110, 2016.
, « Sex-dependent effects of chromogranin B P413L allelic variant as disease modifier in amyotrophic lateral sclerosis. », Hum Mol Genet, 2016.
, « Sex-dependent effects of chromogranin B P413L allelic variant as disease modifier in amyotrophic lateral sclerosis. », Hum Mol Genet, vol. 25, nᵒ 21, p. 4771-4786, 2016.
, « CD11b+Ly6G- myeloid cells mediate mechanical inflammatory pain hypersensitivity. », Proc Natl Acad Sci U S A, vol. 112, nᵒ 49, p. E6808-17, 2015.
, « Dissociation of Axonal Neurofilament Content from Its Transport Rate. », PLoS One, vol. 10, nᵒ 7, p. e0133848, 2015.
, « Early and persistent abnormal decoding by glial cells at the neuromuscular junction in an ALS model. », J Neurosci, vol. 35, nᵒ 2, p. 688-706, 2015.
, « Early-stage treatment with Withaferin A reduces levels of misfolded superoxide dismutase 1 and extends lifespan in a mouse model of amyotrophic lateral sclerosis. », Neurotherapeutics, vol. 12, nᵒ 1, p. 217-33, 2015.
, « Functions of neurofilaments in synapses. », Mol Psychiatry, vol. 20, nᵒ 8, p. 915, 2015.
, « Inflammation Induces TDP-43 Mislocalization and Aggregation. », PLoS One, vol. 10, nᵒ 10, p. e0140248, 2015.
, « Neurofilament subunits are integral components of synapses and modulate neurotransmission and behavior in vivo. », Mol Psychiatry, vol. 20, nᵒ 8, p. 986-94, 2015.
, « Type II spiral ganglion afferent neurons drive medial olivocochlear reflex suppression of the cochlear amplifier. », Nat Commun, vol. 6, p. 7115, 2015.
, « Ubiquilin-2 drives NF-κB activity and cytosolic TDP-43 aggregation in neuronal cells. », Mol Brain, vol. 8, nᵒ 1, p. 71, 2015.
, « Adeno-associated virus-mediated delivery of a recombinant single-chain antibody against misfolded superoxide dismutase for treatment of amyotrophic lateral sclerosis. », Mol Ther, vol. 22, nᵒ 3, p. 498-510, 2014.
, « Interaction of transactive response DNA binding protein 43 with nuclear factor κB in mild cognitive impairment with episodic memory deficits. », Acta Neuropathol Commun, vol. 2, p. 37, 2014.
, « Loss of glial neurofascin155 delays developmental synapse elimination at the neuromuscular junction. », J Neurosci, vol. 34, nᵒ 38, p. 12904-18, 2014.
, « Axonal transport deficits and neurodegenerative diseases. », Nat Rev Neurosci, vol. 14, nᵒ 3, p. 161-76, 2013.
